Video-assisted thoracoscopic cardiac sympathetic denervation for prolonged QT syndrome—a case report

Abstract

Congenital long QT syndrome (LQTS) is a rare genetic disorder associated with multiple mutations causing life-threatening cardiac arrhythmias and sudden death. The treatment of choice for LQTS is therapy with beta blockers. Individuals for whom beta blockers are unsuccessful may be treated by implantable automatic cardioverter defibrillator or left cardiac sympathetic denervation . Video-assisted thoracoscopic left cardiac sympathetic denervation is a simple and minimally invasive technique that results in good long-term benefits in patients with congenital long QT syndromes. Although there is substantial literature about this therapy in adults, few reports detail the outcomes in children who undergo left thoracoscopic sympathectomy to treat LQTS.

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